PEComa. Literature review and case report
Abstract
The family of mesenchymal tumors called PEComas (Perivascular Epithelioid Cell Tumors) has been included in the international Classification of Soft Tissue and Bone Tumors since 2002. Literature review confirms difficulties of timely diagnosis and absence of progress in the treatment results. in spite of advances in research of PEComas histological nature of these tumors is still unclear. Further research of prognostic factors is needed to give proper treatment. Patients with PEComas of different primary sites require close follow-up after the treatment irrespective of malignant potential of tumors, as late recurrence and metastases are possible. This paper presents a case report of 11-year-old girl with vaginal PEComa, who is disease-free 10 years after the treatment.
About the Authors
I. V. Nechushkina
Pediatric Oncology & Hematology Research institute, N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russian Federation
Russian Federation
Russian Federation
Moscow
A. I. Karseladze
Clinical Oncology Research institute, N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russian Federation
Russian Federation
Russian Federation
Moscow
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Nechushkina I.V., Karseladze A.I. PEComa. Literature review and case report. Bone and soft tissue sarcomas, tumors of the skin. 2016;(2):32-43. (In Russ.)
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