Secondary chondrosarcoma of pelvis. Case report and review of literature
Abstract
Secondary chondrosarcoma is a distinctive type of tumor that arises from cartilage lesion. Frequently it has a connection with single or multiple osteochondromas. Some cases arise from other diseases, such as Maffucci Syndrome and Ollier’s disease. A sharp increase in the size of the «cartilaginous cap» osteochondromas is a sign of transformation into a secondary chondrosarcoma. However, there is no strict restriction on the thickness of the «cartilaginous cap», which can be considered pathognomonic malignancy. The overall survival rate for 5 years is approximately 90%. Surgical resection with wide margins is the best treatment option, but local recurrence remains a significant problem in about 10–20% of patients. Patients with secondary pelvic chondrosarcoma are particularly at risk of local recurrence.
About the Authors
E. R. Musaev
FGBU «National Medical Research Center of Oncology named after N.N. Blokhin» of the Ministry of Health of Russia
Russian Federation
Russian Federation
Moscow
D. I. Sofronov
FGBU «National Medical Research Center of Oncology named after N.N. Blokhin» of the Ministry of Health of Russia
Russian Federation
Russian Federation
Moscow
E. A. Sushentsov
FGBU «National Medical Research Center of Oncology named after N.N. Blokhin» of the Ministry of Health of Russia
Russian Federation
Russian Federation
Moscow
N. S. Babkin
FGBU «National Medical Research Center of Oncology named after N.N. Blokhin» of the Ministry of Health of Russia
Russian Federation
Russian Federation
Moscow
A. V. Fedorova
FGBU «National Medical Research Center of Oncology named after N.N. Blokhin» of the Ministry of Health of Russia
Russian Federation
Russian Federation
Moscow
S. A. Shipakhin
FGBU «National Medical Research Center of Oncology named after N.N. Blokhin» of the Ministry of Health of Russia
Russian Federation
Russian Federation
Moscow
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Review
For citations:
Musaev E.R., Sofronov D.I., Sushentsov E.A., Babkin N.S., Fedorova A.V., Shipakhin S.A. Secondary chondrosarcoma of pelvis. Case report and review of literature. Bone and soft tissue sarcomas, tumors of the skin. 2017;(4):17-22. (In Russ.)
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