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Bone and soft tissue sarcomas, tumors of the skin

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Clinical case of treatment of secondary chondrosarcoma developed due to Ollier disease

https://doi.org/10.17650/2219-4614-2023-15-1-66-71

Abstract

Ollier disease is a rare non-hereditary disorder of the bone tissue characterized by development of multiple benign bone tumors – enchondromas. One of the dangerous complications of this pathology is tumor transition into chondrosarcoma. Currently, there are no drug therapies for Ollier disease. Surgical treatment is performed in case of complications (chondrosarcoma, pathological fracture).

The article presents a clinical case of chondrosarcoma treatment  in a 42-year-old male with Ollier disease diagnosed when the patient was 8 years old. Since 2021, the patient noted intensive tumor growth on the right foot and left calf. In August of 2022, the patient sought medical help at the Republican Clinical Oncological Dispensary of the Bashkortostan Ministry of Health. Examination showed synchronous malignant transformation of enchondromas of the right foot and left calf confirmed by histological exam. Due to tumor advancement, surgical treatment  was performed. Other enchondroma lesions are being watched.

About the Authors

M. M. Zamilov
Republican Clinical Oncological Dispensary, Ministry of Health of Republic of Bashkortostan
Russian Federation

Marat M. Zamilov.

73/1 Prospekt Oktyabrya, Ufa 450054, Republic of Bashkortostan



K. V. Menshikov
Republican Clinical Oncological Dispensary, Ministry of Health of Republic of Bashkortostan; Bashkir State Medical University, Ministry of Health of Russia
Russian Federation

73/1 Prospekt Oktyabrya, Ufa 450054, Republic of Bashkortostan; 3 Lenin St., Ufa 450008, Republic of Bashkortostan



Sh. I. Musin
Republican Clinical Oncological Dispensary, Ministry of Health of Republic of Bashkortostan; Bashkir State Medical University, Ministry of Health of Russia
Russian Federation

73/1 Prospekt Oktyabrya, Ufa 450054, Republic of Bashkortostan; 3 Lenin St., Ufa 450008, Republic of Bashkortostan



A. V. Sultanbayev
Republican Clinical Oncological Dispensary, Ministry of Health of Republic of Bashkortostan
Russian Federation

73/1 Prospekt Oktyabrya, Ufa 450054, Republic of Bashkortostan



I. A. Sharifgaliev
Republican Clinical Oncological Dispensary, Ministry of Health of Republic of Bashkortostan; Bashkir State Medical University, Ministry of Health of Russia
Russian Federation

73/1 Prospekt Oktyabrya, Ufa 450054, Republic of Bashkortostan; 3 Lenin St., Ufa 450008, Republic of Bashkortostan



S. V. Osokin
Republican Clinical Oncological Dispensary, Ministry of Health of Republic of Bashkortostan
Russian Federation

73/1 Prospekt Oktyabrya, Ufa 450054, Republic of Bashkortostan



V. S. Chalov
Republican Clinical Oncological Dispensary, Ministry of Health of Republic of Bashkortostan
Russian Federation

73/1 Prospekt Oktyabrya, Ufa 450054, Republic of Bashkortostan



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Review

For citations:


Zamilov M.M., Menshikov K.V., Musin Sh.I., Sultanbayev A.V., Sharifgaliev I.A., Osokin S.V., Chalov V.S. Clinical case of treatment of secondary chondrosarcoma developed due to Ollier disease. Bone and soft tissue sarcomas, tumors of the skin. 2023;15(1):66-71. (In Russ.) https://doi.org/10.17650/2219-4614-2023-15-1-66-71

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ISSN 2219-4614 (Print)
ISSN 2782-3687 (Online)